Severe myoclonic epilepsy in infancy (SME) was described by Dravet in 1978 (1). In 1992,
there were at least 192 published cases (2). At present, it is more difficult to give a precise�…

Severe myoclonic epilepsy in infancy (SMEI) is a rare disease, characterized by febrile and
afebrile, generalized and unilateral, clonic or tonic–clonic seizures that occur in the first year�…

Dravet syndrome was described in 1978 by Dravet (1978) under the name of severe
myoclonic epilepsy in infancy (SMEI). The characteristics of the syndrome were confirmed�…

To report the authors' experience with diagnosis and management of Dravet syndrome, or
severe myoclonic epilepsy in infancy, in the era of commercially available genetic testing�…

Severe Myoclonic Epilepsy in infancy (SMEI, or Dravet syndrome) is a drug‐resistant
epilepsy that occurs in the first year of life of previously healthy children. The main clinical�…

Severe myoclonic epilepsy of infancy (SMEI) is a complex form of epilepsy that was first
described in France in 1978. Because the myoclonic component of this epilepsy is not�…

Aims of our study were to describe the early clinical features of Dravet syndrome (SMEI) and
the neurological, cognitive and behavioral outcome. The clinical history of 37 patients with�…

Purpose: We intended to elucidate the whole clinical course of Dravet syndrome (DS)
comprehensively, from infancy through adulthood. Methods: Subjects were 31 patients with�…

Severe myoclonic epilepsy in infants (SME) is one of the most malignant epileptic
syndromes recognized in the latest classification of epileptic syndromes. The clinical details�…

Dravet syndrome is a severe infantile-onset epilepsy syndrome with a distinctive but
complex electroclinical presentation. A healthy, developmentally normal infant presents at�…