The natural history of idiopathic pulmonary fibrosis (IPF) has been characterized as a
steady, predictable decline in lung function over time. Recent evidence suggests that some�…

Background The clinical course of patients with idiopathic pulmonary fibrosis (IPF) is
generally marked by a decline in pulmonary function over time. Increasingly, patients have�…

Acute exacerbation of idiopathic pulmonary fibrosis has been defined as an acute, clinically
significant, respiratory deterioration of unidentifiable cause. The objective of this�…

The goal of this review is to summarise the clinical features, management, and prognosis of
acute exacerbations of idiopathic pulmonary fibrosis (AE-IPF). AE-IPF has previously been�…

Although acute exacerbation of idiopathic pulmonary fibrosis (IPF) has become well
recognised, the reported incidence and outcomes are highly variable, and risk factors are�…

Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive fibrosing lung disorder of
unknown aetiology whose diagnosis involves the careful exclusion of secondary causes for�…

Background: Acute exacerbation is a substantial cause of death in patients with idiopathic
pulmonary fibrosis with poorly described prognostic factors. Objectives: To review the�…

Patients with idiopathic pulmonary fibrosis (IPF) inevitably experience declines in functional
status that are most frequently due to progressive pulmonary fibrosis. However, the cause of�…

It is hypothesized that the extent and severity of fibrosis and cellularity found on lung biopsy
determine the prognosis and response to therapy in idiopathic pulmonary fibrosis (IPF). The�…

Rationale: The serial computed tomography findings and prognosis of the acute
exacerbation of idiopathic pulmonary fibrosis (IPF) are not yet well defined in a larger�…