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Case Reports
. 2016 Mar 5;2(2):128-31.
doi: 10.1016/j.jdcr.2015.10.010. eCollection 2016 Mar.

Diverse cutaneous manifestations of Erdheim-Chester disease in a woman with a history of Langerhans cell histiocytosis

Julia Pettersen Neckman  1 , Joyce Kim  2 , Mahan Mathur  3 , Peggy Myung  1 , Michael Girardi  1
Affiliations
Case Reports

Diverse cutaneous manifestations of Erdheim-Chester disease in a woman with a history of Langerhans cell histiocytosis

Julia Pettersen Neckman et al. JAAD Case Rep. .
No abstract available

Keywords: BRAF V600E mutation; ECD, Erdheim-Chester disease; Erdheim-Chester disease; LCH, Langerhans cell histiocytosis; PET-CT, Positron emission tomography–computerized tomography; non–Langerhans cell histiocytosis.

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Figures

Fig 1
Fig 1
Clinical photographs of ECD.
Fig 2
Fig 2
Histology photographs of ECD. (A, Hematoxylin-eosin stain; original magnification: ×20. B, CD1a stain; original magnification ×20. C, S-100 stain; original magnification: ×20.)
Fig 3
Fig 3
Characteristic radiographic findings of ECD from PET-CT. A, CT image shows bilateral osteosclerotic changes of the femur and tibia. B, PET image with FDG uptake in the bilateral femur and tibia.
See this image and copyright information in PMC

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